Abstract

CARRERAS CALVO, Fernando; CASTELLANOS ROJAS, Rolando; PEROZO PANICELLO, Rut  and  RAMIREZ LANA, Lázaro. Long QT syndrome and sudden cardiovascular death. AMC [online]. 2015, vol.19, n.3, pp.279-287. ISSN 1025-0255.

Background: long QT syndrome is an arrhythmogenic canalopathy characterized by a serious alteration in the ventricular repolarization, translated electrocardiographically by a prolongation of the QT interval that predispose to sudden death caused by malignant ventricular arrhythmias tracing in torsades de pointes. Objective: to present the clinical case of a patient with this syndrome that is infrequent in our environment. Clinical case: a thirty-one-year-old patient with antecedents of being a healthy person, who was admitted in the hospital twice during her pregnancy because of high arterial pressure in 2013. The patient presented syncope manifestations from which she recovered spontaneously. In January 2014, the patient is admitted in the hospital with dyspeptic disorders and epigastralgia. After being admitted, the patient presented syncope manifestations and ventricular tachycardia exhibited on the electrocardiogram tracing in torsades de pointes and cardiac arrest. It was necessary to perform a cardiopulmonary resuscitation and endotracheal intubation. The patient presented this combination of manifestations for 48 hours. She is sent to the Cardiology Institute of Havana where she is studied by the arrhythmia medical team and the implantation of an implantable cardioverter-defibrillator is decided.

Keywords : LONG QT SYNDROME; CHANNELOPATHIES; DEATH, SUDDEN, CARDIAC; ADULT; CASE REPORTS.

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