Abstract

SANCHEZ LINARES, Vladimir et al. No bullous congenital ichthyosiform erythroderma associated to vegetating pemphigus. Case presentation. Gac Méd Espirit [online]. 2016, vol.18, n.1, pp. 84-90. ISSN 1608-8921.

Background: The non-bullous  congenital ichthyosiform erythroderma is a genodermatosis that is present from the birth and the vegetating pemphigus  is a bullous disease that occurs at early ages of life, the clinical manifestations of these entities are different, both are uncommon when they are presented in isolation, much more when they appear in a patient Objective: To describe the case of a patient with a non-bullous congenital ichthyosiform erythroderma and vegetating pemphigus a strange clinical situation for their incidence. Case presentation: Patient of 28 years, with antecedents of suffering of non-bullous congenital ichthyosiform erythroderma that began to develop blisters and when breaking they left erosions that later gave place to hypertrophic and papillomatous vegetation.  To arrive to the diagnosis was kept in mind the clinical approach and the histopathology. Conclusions: The non-bullous congenital ichthyosiform erythroderma and the vegetating pemphigus are uncommon entities in the medical practice, much more when both are presented in a patient.

Keywords : The non-bullous congenital ichthyosiform erythroderma; ichthyosis lamelar; vegetating pemphigus.