Introduction:

Systemic sclerosis is a rare disease for which there is limited information in the Reference Center for Rheumatic Diseases of Havana.

Objective:

To describe the clinical-epidemiological characteristics of the patients treated with this diagnosis in the period from November 2017 to March 2019.

Methods:

A descriptive, cross-sectional observational study was carried out in 73 patients. Sociodemographic variables such as age, sex, skin color, educational level and occupation, clinical variables such as form of presentation and time of diagnosis of the disease, clinical manifestations, associated comorbidities and treatment were evaluated.

Results:

57.5% presented the diffuse form of the disease and 48.8% had more than 10 years of diagnosis. Digestive involvement in 94.5%, osteomyoarticular disease in 89.0%, and cardiovascular disease in 87.7% were the most represented by organs and systems.

Conclusions:

The diffuse form of the disease predominated, patients with more than 10 years of diagnosis and skin, digestive and osteomyoarticular involvement. HT followed by fibromyalgia were the most identified comorbidities. Anti-calcium, ACEI, steroids and Methotrexate were the drugs most used in treatment.

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